Category Archives: Genetic Disorders

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Urifresh Capsules Get Rid of Stinky Urine

 

 

 

Diabetes & Stinky Urine
Diabetes Main Page
Diabetes
Ketoacidosis

 

Genetic Disorders that Can Cause Foul Smelling Urine
Genetic Disorders Main Page
Glycogen Storage Diseases
Maple Syrup Urine Disease
Phenylketonuria
Renal Glycosuria

 

Substances that Cause Stinky Urine
Habits and Substances Main Page
Dehydration
Foods, Drinks and Spices
High Protein, Low-Carb Diets
Medications
Smoking
Vitamins and Supplements

 

Infections that May Make Your Urine Smell Bad
Infections Main Page
Sexually Transmitted Diseases (STDs)
Urinary Tract Infections (UTIs)
Yeast Infections

 

Ketonuria & Ketones-Related Causes of Stinky Urine
Ketonuria Main Page
Eating Disorders
Extreme Stress or Illness
Fasting
Glycogen Storage Disease
High Protein, Low-Carb Diets
Hyperthyroidism
Pregnancy and Lactation
Renal Glycosuria
Repeated Vomiting
Starvation

 

Kidney, Bladder and Liver Conditions that Cause Smelly Urine
Kidney, Bladder and Liver Conditions Main Page
Bladder Cancer
Fistula
Kidney Stones
Liver Failure
Renal Glycosuria
Vesicoureteral Reflux

 

Top 10 Causes of Stinky Urine
Asparagus
Dehydration
High Protein, Low-Carb Diets
Kidney Stones
Medications
Sexually Transmitted Diseases (STDs)
Smoking
Urinary Tract Infections (UTI)
Vitamins and Supplements
Yeast Infections

 

Worst Case Scenarios
Worst Case Scenarios Main Page
Bladder Cancer
Diabetes
Fistula
Glycogen Storage Disease
Ketoacidosis
Liver Failure
Maple Syrup Urine Disease
Phenylketonuria

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Filed under Bladder & Liver Diseases, Colors of Urine, Genetic Disorders, Infections, Ketone-Related, Kidney, Top 10 Causes of Stinky Urine

​Causes of Smelly Urine Related to Ketones

High Protein, Low Carb Diets

Eating a diet high in protein puts your liver to work. As your liver processes the extra protein you’ve taken in, it produces am
monia as a by-product.  Since ammonia is toxic, your liver converts it to urea…MORE..

 

 

 

Eating Disorders

 

The eating disorders Anorexia and Bulimia can cause stinky urine in a couple of different ways.  One way is from starvation causing an excess of ketones in the blood.  In the case of bulimia, repeated vomiting may also contribute to foul smelling urine…MORE..

 

Starvation

Starvation can cause the body to go into ketosis.  The above-average level of ketones in the blood may cause stinky urine.

 

Fasting

Fasting, like starvation and eating disorders, can cause your body to go into ketosis.  While fasting, you may notice that your urine smells bad.  The reason is that your body is eliminating ketones from your blood, and they don’t smell very good.

Glycogen Storage Disease

 

Glycogen storage disease type 1, or GSDI or von Gierke disease, is a genetic disorder.  That means that if your parents or grandparents had it, you may be at risk.  It starts early, when you’re still an infant, and it can lead to problems with growth later in life. MORE.. 

 

Renal Glycosuria

Renal glycosuria is a very rare inherited disease, estimated to affect just 0.16-6.3% of the population.  Although the condition is benign, which means that people who have it don’t have many problems, it can make your urine smell bad.MORE..

 

 

Pregnancy and Lactation

 

Hormonal changes during pregnancy or lactation can cause stinky urine.  However, another possible reason you are noticing extremely smelly urine while you’re pregnant may be the changes in your own sense of smell…once again, due to hormones.

 

Extreme Stress or Illness

 

There are many ways that extreme stress or illness can cause stinky urine, but the most common is the change in your body’s hormones.  Your body may start operating differently under extreme stress, causing all sorts of problems, including smelly pee.

 


Repeated Vomiting

C’mon…you don’t want to see a photo for that, do you?  Have a daisy instead.

 

Hyperthyroidism

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Genetic Disorders that Cause Stinky Urine

Maple Syrup Urine Disease 


Maple Syrup Urine Disease, or branched-chain ketoaciduria, is a rare genetic disease that causes problems with metabolizing branched chain amino acids. It causes a baby’s urine to smell like maple syrup or burnt sugar. MORE..

Phenylketonuria

 

Phenylketonuria, also known as PKU, is a rare genetic disorder that may cause smelly urine.  The smell is often described as “mousy” or “musty” and is usually detected not only in urine, but in body odor and breath as well. MORE..

 

Glycogen Storage Disease

 

Glycogen storage disease type 1, or GSDI or von Gierke disease, is a genetic disorder.  That means that if your parents or grandparents had it, you may be at risk. 

 

It starts early, when you’re still an infant, and it can lead to problems with growth later in life.  If left unchecked and untreated, it could lead to problems with glycogen being stored as fat, which can prove fatal.MORE..

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